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Crow Fukase Syndrome

《英文msh詞典》Crow Fukase Syndrome
[入口詞] Crow Fukase Syndrome
[主題詞] POEMS Syndrome
[英文釋義] A multisystemic disorder characterized by a sensorimotor polyneuropathy (POLYNEUROPATHIES),organomegaly,endocrinopathy,monoclonal gammopathy,and pigmentary skin changes. Other clinical features which may be present include EDEMA; CACHEXIA; microangiopathic glomerulopathy; pulmonary hypertension (HYPERTENSION,PULMONARY); cutaneous necrosis; THROMBOCYTOSIS; and POLYCYTHEMIA. This disorder is frequently associated with osteosclerotic myeloma. (From Adams et al.,Principles of Neurology,6th ed,p1335; Rev Med Interne 1997;18(7):553-62)